KMID : 1130320100530110975
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Korean Journal of Pediatrics 2010 Volume.53 No. 11 p.975 ~ p.978
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Perivascular epithelioid cell tumor (PEComa) of the ascending colon: the implication of IFN-¥á2b treatment
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Park Sun-Ju
Han Dong-Kyun Baek Hee-Jo Chung Sang-Young Nam Jong-Hee Kook Hoon Hwang Tai-Ju
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Abstract
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A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PEComa). PEComa in the colon is very rare. Only a few cases have been reported so far. An effective treatment method for this rare tumor has not been established yet. The patient received adjuvant interferon-¥á immunotherapy for 1 year. He has been tumor-free for 26 months since the initial diagnosis. This report is the first documented case of the use of interferon-¥á for pediatric PEComa of the colon.
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KEYWORD
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Perivascular epithelioid cell tumor, PEComa, Colon, Interferon-alpha
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